Recurrent haemoptysis: a rare diagnosis of kaposiform lymphangiomatosis and review of literature

Roukhama Fedidat; Anna Elia; Alon Hershko; Zvi Fridlender

doi:10.1136/bcr-2022-250825

Recurrent haemoptysis: a rare diagnosis of kaposiform lymphangiomatosis and review of literature

Roukhama Fedidat, Anna Elia, Alon Hershko, Zvi Fridlender^*

^*Corresponding author for this work

Research output: Contribution to journal › Review article › peer-review

Abstract

Kaposiform lymphangiomatosis (KLA) is a rare clinicopathological entity among lymphatic anomalies. The main involved sites are the mediastinum and the lungs but the disease can also affect multiple extrathoracic organs. Little is known about the pathophysiology, the natural history, the treatment response and the long-term outcome of this disorder. KLA is typically diagnosed in childhood. We present here the case of an adult man with 13 years recurrent episodes of haemoptysis who was finally found to suffer from KLA. Following this, we present a comprehensive review of the literature.

Original language	English
Article number	e250825
Journal	BMJ Case Reports
Volume	15
Issue number	9
DOIs	https://doi.org/10.1136/bcr-2022-250825
State	Published - 28 Sep 2022
Externally published	Yes

Keywords

malignant and benign haematology
respiratory medicine

UN SDGs

This output contributes to the following UN Sustainable Development Goals (SDGs)

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10.1136/bcr-2022-250825

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title = "Recurrent haemoptysis: a rare diagnosis of kaposiform lymphangiomatosis and review of literature",

abstract = "Kaposiform lymphangiomatosis (KLA) is a rare clinicopathological entity among lymphatic anomalies. The main involved sites are the mediastinum and the lungs but the disease can also affect multiple extrathoracic organs. Little is known about the pathophysiology, the natural history, the treatment response and the long-term outcome of this disorder. KLA is typically diagnosed in childhood. We present here the case of an adult man with 13 years recurrent episodes of haemoptysis who was finally found to suffer from KLA. Following this, we present a comprehensive review of the literature.",

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AU - Fedidat, Roukhama

AU - Elia, Anna

AU - Hershko, Alon

AU - Fridlender, Zvi

N1 - Publisher Copyright: © BMJ Publishing Group Limited 2022. No commercial re-use. See rights and permissions. Published by BMJ.

PY - 2022/9/28

Y1 - 2022/9/28

N2 - Kaposiform lymphangiomatosis (KLA) is a rare clinicopathological entity among lymphatic anomalies. The main involved sites are the mediastinum and the lungs but the disease can also affect multiple extrathoracic organs. Little is known about the pathophysiology, the natural history, the treatment response and the long-term outcome of this disorder. KLA is typically diagnosed in childhood. We present here the case of an adult man with 13 years recurrent episodes of haemoptysis who was finally found to suffer from KLA. Following this, we present a comprehensive review of the literature.

AB - Kaposiform lymphangiomatosis (KLA) is a rare clinicopathological entity among lymphatic anomalies. The main involved sites are the mediastinum and the lungs but the disease can also affect multiple extrathoracic organs. Little is known about the pathophysiology, the natural history, the treatment response and the long-term outcome of this disorder. KLA is typically diagnosed in childhood. We present here the case of an adult man with 13 years recurrent episodes of haemoptysis who was finally found to suffer from KLA. Following this, we present a comprehensive review of the literature.

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KW - respiratory medicine

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ER -

Recurrent haemoptysis: a rare diagnosis of kaposiform lymphangiomatosis and review of literature

Abstract

Keywords

UN SDGs

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