Osteopathia striata, cranial sclerosis with cleft palate and facial nerve palsy

L. Kornreich*, M. Grunebaum, N. Ziv, A. Shuper, M. Mimouni

*Corresponding author for this work

Research output: Contribution to journalArticlepeer-review

24 Scopus citations

Abstract

Osteopathia striata (OS) is a rare bone dysplasia characterized by longitudinal sclerotic striations of the long bones. It is of no clinical importance, but OS associated with cranial sclerosis represents a separate entity with a high incidence of palatine malformations and deafness. Only 19 cases of this entity have been reported in the literature. One patient of this series also had facial nerve paralysis. This paper presents a second case of OS, cranial sclerosis, palatine pathology and recurrent facial nerve paralysis. This incidence of 2/20 (10%) does not seem to be coincidental but raises the possibility that facial nerve palsy is one of the clinical manifestations of this specific bone abnormality.

Original languageEnglish
Pages (from-to)101-103
Number of pages3
JournalEuropean Journal of Pediatrics
Volume147
Issue number1
DOIs
StatePublished - Jan 1988

Keywords

  • Bone
  • Cranial sclerosis
  • Osteopathia striata

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