Abstract
A new entity manifested by severe congenital neutropenia associated with osteoporosis and recurrent bone fracture is described in a family. A possible role for a new recognized cytokine system involved in bone remodeling, the osteoprotegerin/receptor activator of nuclear factor-κB ligand, is suggested.
Original language | English |
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Pages (from-to) | 34-37 |
Number of pages | 4 |
Journal | American Journal of Hematology |
Volume | 72 |
Issue number | 1 |
DOIs | |
State | Published - 1 Jan 2003 |
Externally published | Yes |
Keywords
- Immunodeficiency
- Neutropenia
- Osteoporosis