Caroli’s disease was complicated by a Budd-Chiari-like syndrome as a result of enlarged lymph nodes that compressed the vena cava. Histologically the picture was compatible with “sinus histiocytosis with massive lymphadenopathy.” We discuss the combination of these two rare disorders.
- Budd-chiari-like syndrome
- Caroli’s disease
- Sinus histiocytosis with massive lymphadenopathy