TY - JOUR
T1 - A perfect mimic
T2 - the role of multimodality imaging in right ventricular cardiomyopathy - A case report
AU - Viskin, Dana
AU - Laufer-Perl, Michal
AU - Topilsky, Yan
AU - Banai, Shmuel
AU - Khoury, Shafik
N1 - Publisher Copyright:
© The Author(s) 2024. Published by Oxford University Press on behalf of the European Society of Cardiology.
PY - 2024/12/1
Y1 - 2024/12/1
N2 - Background Distinguishing right ventricular cardiac sarcoidosis (RVCS) from arrhythmogenic right ventricular cardiomyopathy (ARVC) is often a challenging task particularly when imaging findings are limited to the right ventricle and when electrocardiographic and arrhythmic findings are typical for ARVC. Here, we discuss the challenges of diagnosis and management in a patient whose initial work-up strongly suggested ARVC and was later diagnosed with cardiac sarcoidosis (CS), highlighting the role of multimodality imaging Case summary On presentation, this patient displayed electrocardiographic abnormalities, arrhythmia morphology, and cardiac magnetic resonance imaging findings consistent with the criteria for a definite diagnosis of ARVC. However, through the use of multimodal imaging, a final diagnosis of CS was made. Subsequent immunosuppressive treatment effectively managed the inflammation, and as a primary prevention measure, an implantable cardioverter-defibrillator was implanted. Almost 2 years following the initial presentation, the patient received an appropriate shock from the device, attributed to rapid ventricular tachycardia arising from myocardial scarringDiscussion Right ventricular cardiac sarcoidosis can closely resemble ARVC, making it challenging to distinguish between the two. Multimodality imaging is pivotal for accurate diagnosis and risk assessment, as well as for adjusting immunosuppressive therapy and monitoring response to treatment in CS.
AB - Background Distinguishing right ventricular cardiac sarcoidosis (RVCS) from arrhythmogenic right ventricular cardiomyopathy (ARVC) is often a challenging task particularly when imaging findings are limited to the right ventricle and when electrocardiographic and arrhythmic findings are typical for ARVC. Here, we discuss the challenges of diagnosis and management in a patient whose initial work-up strongly suggested ARVC and was later diagnosed with cardiac sarcoidosis (CS), highlighting the role of multimodality imaging Case summary On presentation, this patient displayed electrocardiographic abnormalities, arrhythmia morphology, and cardiac magnetic resonance imaging findings consistent with the criteria for a definite diagnosis of ARVC. However, through the use of multimodal imaging, a final diagnosis of CS was made. Subsequent immunosuppressive treatment effectively managed the inflammation, and as a primary prevention measure, an implantable cardioverter-defibrillator was implanted. Almost 2 years following the initial presentation, the patient received an appropriate shock from the device, attributed to rapid ventricular tachycardia arising from myocardial scarringDiscussion Right ventricular cardiac sarcoidosis can closely resemble ARVC, making it challenging to distinguish between the two. Multimodality imaging is pivotal for accurate diagnosis and risk assessment, as well as for adjusting immunosuppressive therapy and monitoring response to treatment in CS.
KW - ARVC
KW - Case report
KW - Right ventricular cardiomyopathy
KW - Sarcoidosis
UR - http://www.scopus.com/inward/record.url?scp=85212954634&partnerID=8YFLogxK
U2 - 10.1093/ehjcr/ytae664
DO - 10.1093/ehjcr/ytae664
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AN - SCOPUS:85212954634
SN - 2514-2119
VL - 8
JO - European Heart Journal - Case Reports
JF - European Heart Journal - Case Reports
IS - 12
M1 - ytae664
ER -